The Turkish Journal of Pediatrics 2010 , Vol 52 , Num 6
Reye Syndrome and Liver Transplantation
department of Liver Diseases, Gastroenterologie Surgery and Multiorgan Transplantation, Multiorgan Transplantation Unit, Hautepierre Hospital, University of Strasbourg, Strasbourg, and 2Hepato-Gastro-Enterology Service, Hospices Civils de Colmar, Colmar, France Çag M, Saouli A-C, Audet M, Wolf P, CinqualbreJ. Reye syndrome and liver transplantation. Turk J Pediatr 2010;52: 662-664.

Reye syndrome is a rare, but severe and often fatal disease. The etiology of the classical Reye syndrome is unknown, but it is typically preceded by a viral infection with a free interval of three to five days. The main physiopathological hypothesis is a mitochondrial metabolism insult causing acute liver failure and encephalopathy. Survivors present serious neurological sequelae. The treatment of Reye syndrome is usually medical with intensive care management. Herein, we present the clinical case of a six-month-old baby diagnosed with Reye syndrome with a fulminant hepatitis, who was successfully liver transplanted with an auxiliary partial orthotopic liver transplantation. Keywords : Reye syndrome, fulminant hepatitis, auxiliary partial orthotopic liver transplantation, pediatric liver transplantation, aspirin.

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