The Turkish Journal of Pediatrics 2008 , Vol 50 , Num 1
Acute myocardial infarction and ascending aortic aneurysm in a child with Behçet’s disease
1Department of Pediatric Cardiology, Guangdong Provincial Cardiovascular Institute, Guangzhou, China
2Department of Rheumatology, Guangdong Provincial People’s Hospital, Guangzhou, China
3Department of Pediatrics, Guangdong Provincial People’s Hospital, Guangzhou, China
Zhuang J, Wang S, Zhang Z, Zeng S, Shi Y, Nong S. Acute myocardial infarction and ascending aortic aneurysm in a child with Behçet’s disease. Turk J Pediatr 2008; 50: 81-85.

A 12-year-old boy with a history of recurrent aphthous ulcerations and cutaneous erythema nodosum suddenly experienced chest pain. Together, the symptoms and a positive skin pathergy test established a diagnosis of Behçet’s disease. An acute extensive anterior myocardial infarction was based on electrocardiography and a cardiac computed tomography confirmed an ascending aortic aneurysm. Coronary angiography showed mural irregularity and a 50% constriction in the first diagonal artery. Following treatment with urokinase, corticosteroids, colchicine, and aspirin, most symptoms gradually improved. There were no complications noted at the one-year follow-up evaluation. Myocardial infarction is a rare event in children with Behçet’s disease; treatment with corticosteroids and colchicine can result in regression of concomitant aneurysm. Keywords : Behçet’s disease, myocardial infarction, aortic aneurysm, child

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