The Turkish Journal of Pediatrics 2007 , Vol 49 , Num 3
Successful treatment of retroperitoneal giant cell-type malignant fibrous histiocytoma in a 5-year-old boy
1Departments of Pediatrics, Dr. Burhan Nalbantoğlu State Hospital, Nicosia, North Cyprus
2Departments of Pediatric Surgery, Dr. Burhan Nalbantoğlu State Hospital, Nicosia, North Cyprus
3Pathology Unit, Department of Pediatrics, Hacettepe University Faculty of Medicine, Ankara, Turkey
Çağlar K, Güngör S, Akansoy S, Sakallı Ü, Orhan D, Çağlar M. Successful treatment of retroperitoneal giant cell-type malignant fibrous histiocytoma in a 5-year-old boy. Turk J Pediatr 2007; 49: 307-311.

Malignant fibrous histiocytoma, usually seen in patients older than 10 years, is an aggressive soft-tissue sarcoma occurring mostly in the extremities and the trunk, but it is extremely rare in children. We report the clinical, radiological and pathologic features of a five-year-old boy who was diagnosed as a retroperitoneally originated malignant fibrous histiocytoma. The patient with unresectable mass was successfully treated with multidisciplinary approach, with chemotherapy, surgery and radiotherapy, by using combined chemotherapy consisting of vincristine, cisplatinum, adriamycin, cyclophosphamide, actinomycin D and dacarbazine. Keywords : giant cell-type malignant fibrous histiocytoma, retroperitoneal, children

Copyright © 2016 turkishjournalpediatrics.org