The Turkish Journal of Pediatrics 2004 , Vol 46 , Num 1
Ectomesenchymoma: case report and review of the literature

Departments of Pathology, Yüzüncü Yıl University Faculty of Medicine, Van, Turkey

Departments of Pediatric Surgery, Yüzüncü Yıl University Faculty of Medicine, Van, Turkey

Abstract

Kösem M, İbiloğlu İ, Bakan V, Köseoğlu B. Ectomesenchymoma: case report and review of the literature. Turk J Pediatr 2004; 46: 82-87.

Ectomesenchymoma (EMCH) is a rare tumor that may arise in the brain or soft tissue. This tumor type is defined as a form including ectodermal components represented by neuroblasts or ganglion cells and differentiated mesenchymal structures of various types. The mesenchymal component is most often a rhabdomyosarcoma, but liposarcoma, malignant fibrous histiocytoma, leiomyosarcoma, chondrosarcoma, malignant schwannoma, and osseous elements have also been recorded. We report a case of an abdominal malignant ectomesenchymoma, containing three components, schwannoma, embryonal rhabdomyosarcoma, and ganglion cells, in a four-month-old infant. We also review 43 previously reported cases.

Keywords : ectomesenchymomarhabdomyosarcomaganglion cellsmalignant schwannoma.
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