The Turkish Journal of Pediatrics 2004 , Vol 46 , Num 3
A case of patent ductus venosus with pulmonary arterio-venous fistula as a rare and unique clinical entity

Department of Pediatric Surgery, Hacettepe University Faculty of Medicine, Ankara, Turkey

Departmens of Radiology, Hacettepe University Faculty of Medicine, Ankara, Turkey

Abstract

Büyükyavuz İ, Ekinci S, Haliloğlu M, Şenocak ME, Çiftçi AÖ. A case of patent ductus venosus with pulmonary arterio-venous fistula as a rare and unique clinical entity. Turk J Pediatr 2004; 46: 272-274.

A 13-year-old boy presenting with digital and lip cyanosis, easy fatigability, and weight gain was diagnosed to have an intrapulmonary arterio-venous fistula. During his routine follow-up examinations, there was fullness on right upper quadrant of his abdomen. Abdominal ultrasonography (USG) showed a mass in portal hilus. We planned abdominal computed (CT) to gain tomography detailed information about the mass. Surprisingly abdominal CT and the color-Doppler sonography showed that the structure mimicking a mass was patent ductus venosus (PDV).

We report PDV with intrapulmonary arterio-venous fistula as a unique and rare clinical entity. In addition, we underline the misdiagnosis of portal mass instead of patent ductus venosus. If there is a portal mass in USG or CT, color- Doppler sonography or, if needed, other diagnostic methods should be used to exclude PDV.

Keywords : portosystemic shunting patent ductus venosus pulmonary arterio-venous fistula hepatic dysfunction hypoxemia.
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