The Turkish Journal of Pediatrics
2012 , Vol 54 , Num 6
Rhabdomyosarcoma of the Common Bile Duct: An Unusual Cause of Obstructive Jaundice in a Child
Departments of 1Pediatric Surgery, and 3Radiology, and 4Pediatric Pathology Unit, Department of Pediatrics, Hacettepe
University Faculty of Medicine, and 2Department of Gastroenterology, Türkiye Yüksek İhtisas Training and Research
Hospital, Ankara, Turkey. E-mail: ikarnak@hacettepe.edu.tr
Biliary rhabdomyosarcoma (RMS) is a rare malignancy of childhood. The
radiological findings and clinical presentation of the tumor can mimic
an entirely different pathology. The incidence of RMS has impeded the
development of a standardized form of treatment. A four-year-old child with
botryoid RMS in the common bile duct is reported herein to emphasize
the role of surgery in the small-sized tumor and the role of endoscopic
retrograde cholangiopancreatography (ERCP) in the diagnosis and relief of
biliary obstruction before total excision.
Keywords :
biliary rhabdomyosarcoma, jaundice, endoscopic retrograde
cholangiopancreatography, botryoid rhabdomyosarcoma, embryonal rhabdomyosarcoma.